Qap (Anatomical Pathology) 

QAP Peer Review

AP209
Case History: M/45 left thigh mass
Intended diagnosis: Extraskeletal myxoid chondrosarcoma. Contributed by:KFT
Code Diagnosis Comment Score
anonymous Extraskeletal myxoid chondrosarcoma (100%) nil  100
anonymous Soft tissue: Extraskeletal myxoid chondrosarcoma nil  100
anonymous Extraskeletal myxoid chondrosarcoma (100%) nil  100
anonymous Extraskeletal myxoid chondrosarcoma, 100% nil  100
anonymous Extraskeletal myxoid chondrosarcoma. 100% X ray, CT or MRI to exclude bone origin. The top differential is parachordoma. More sampling to look for chondroid differentiation eg. lacunar cells to support myxoid chondrosarcoma and physaliferous cells to support parachordoma. For myxoid chondrosarcoma, less than 20% of cases are +ve for S100 while parachordoma is usually +ve for S100 and cytokeratin. Rhabdomyosarcoma(another differential) will be +ve for muscle markers. Myxoid matrix of chondrosarcoma stains with colloidal iron and is hyaluronidase resistant while that of other differential are hyaluronidase sensitive. Myxoid chondrosarcoma can be confirmed by cytogenetics: t(9;22)(q22;q12) balanced translocation.  100
anonymous Extraskeletal myxoid chondrosarcoma. (100%) nil  100
anonymous Thigh, soft tissue tumour - Extraskeletal Chondrosarcoma 100% nil  90
anonymous Extraskeletal myxoid chondrosarcoma (100%) nil  100
anonymous Myxoid chondrosarcoma 100% nil  100
anonymous Extraskeletal myxoid Chrondrosarcoma. nil  100
anonymous SOFT TISSUE mass, left thigh - Extraskeletal MYXOID CHONDROSARCOMA (100%) nil  100
anonymous Extraskeletal myxoid chondrosarcoma nil  100
anonymous Extraskeletal myxoid chondrosarcoma 100% nil  100
anonymous Extraskeletal myxoid chondrosarcoma (100%) Associate with t(9;12)(q22;q12) translocation; one of the soft tissue sarcoma related to EWS gene translocation  100
anonymous Extraskeletal myxoid chondrosarcoma nil  100